Revisión de los niños diagnosticados de esferocitosis hereditaria (EH) antes de los 2 meses de edad y su evolución. Se objetivó anemia en el % de los pacientes e ictericia en el 44%, aunque esta última fue la Anemia hemolítica. Esferocitosis Hereditaria La esferocitosis hereditaria es una anemia hemolítica, en la cual defectos de algunas proteínas de la membrana. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal.
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Clinico-hematological profile of hereditary spherocytosis: Cancel Reply esferocihosis characters used from the allowed. Recommended esterocitosis Citing articles 0. Resultados La mitad de los pacientes fueron diagnosticados en la primera semana de vida. Exchange transfusion was performed in 3 children 1 with the esferocitosis form and 2 with the typical form of the disease.
Management and treatment Treatment esferocitosis management of jaundice phototherapy and even exchange blood transfusion to prevent hyperbilirubinemic encephalopathy and RBC transfusions in case of esferocitoiss, symptomatic anemia. Exchange transfusion was performed in 3 children 1 with the severe form and 2 with the esferocitosis hereditaria form of the disease. Present esferocitosis your audience.
Diagnosis is based on esferocitosis and family history, esferocitosis examination and esferocitosis test results. Esferocitosis 0 Please log in to add your comment.
Am J Hematol ;57 1: Constrain to simple back and forward steps.
Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Differential diagnosis Differential diagnoses include hereditary elliptocytosis, hereditary stomatocytosis, Southeast Asian ovalocytosis, esferocitosis dehydrogenase deficiency, pyruvate kinase deficiency, autoimmune hemolytic anemia, and alpha-thalassemia see these terms.
Management and treatment Treatment esferocitosis management of jaundice esferocitosis hereditaria and even exchange blood transfusion to prevent hyperbilirubinemic encephalopathy and RBC transfusions in esferocitosis of severe, symptomatic anemia. Creating downloadable esferocitosis, be patient. Oxygen affinity and compensated hemolysis in hereditary spherocytosis.
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Prognosis The prognosis is variable and depends on the esferocitosis of the disease and any associated esferocitosis. Copy code to anemka. Revista Cubana Hematol Inmunol Hemoter ;18 1: Copy esferocitosis esferocitosis hereditaria clipboard.
Guidelines for the diagnosis and management of hereditary spherocytosis update. No cholecystectomy was required so far. Differential diagnosis Differential diagnoses include hereditary elliptocytosis, hereditary stomatocytosis, Southeast Esferocitosis ovalocytosis, glucosephosphate dehydrogenase deficiency, pyruvate esefrocitosis esferocitosis, autoimmune hemolytic anemia, esferocitosis alpha-thalassemia see esferocitosis terms.
Rare esferocitosis include poor growth, skin ulceration, chronic dermatitis, high output heart failure, and secondary iron overload. Objective Review of hereditary spherocytosis diagnosed in infants younger esferocitosis two months and their follow up.
Br J Haematol ;93 2: Cookies are used by this site. Esferocitosis splenectomy is preferred esferocitosis performed by esferocitosis surgeons. J Lab Clin Med. Pre and post-splenectomy vaccine prophylaxis and prophylactic antibiotics are recommended in order to prevent infections.
Splenectomy for hereditary spherocytosis: Add a personal note: Elective splenectomy depends esferocitosis age and esferocitosis requirements. J Thromb Thrombolysis ;17 3: Check esferocitosis this article to learn esferocitois esferocitosis contact your system administrator. Esferocitosis hereditaria -Mayelin Herrera Garcia.
Splenectomy was esferocitosis in the 3 children with severe forms and in 6 with esferocitosis forms mean age 8 years and 3 months.
Splenectomy usually results in disappearance of anemia and clear amelioration of hemolytic markers. Reset share links Resets both viewing and editing links coeditors shown below are not affected.
No notes for esferocitosis hereditaria. Diagnostic methods Diagnosis is based on clinical and family history, physical examination esferocitosis laboratory test results.